Kodex

ICD-10-CM-TERMS

Term

maple syrup urine disease

Hierarchy

Disorder (of)
- metabolism NOS
  - amino-acid
    - branched chain
      - 3-methylglutaconic aciduria
      - hyperleucine-isoleucinemia
      - hypervalinemia
      - isovaleric acidemia
      - maple syrup urine disease
      - methylmalonic acidemia
      - organic aciduria NEC
      - other specified
      - propionate NEC
      - propionic acidemia

Long Title

maple syrup urine disease

Disorder (of) metabolism NOS amino-acid branched chain maple syrup urine disease

Codes

E71.0 Maple-syrup-urine disease