kodex

Kodex

C88.3

Immunoproliferative small intestinal disease

Copy Code Send Code

Hierarchy

  • C00-D49 Neoplasms (C00-D49)
    • C00-C96 Malignant neoplasms (C00-C96)
      • C81-C96 Malignant neoplasms of lymphoid, hematopoietic and related tissue (C81-C96)
        • C88 Malignant immunoproliferative diseases and certain other B-cell lymphomas
          • C88.0 Waldenström macroglobulinemia
          • C88.2 Heavy chain disease
          • C88.3 Immunoproliferative small intestinal disease
          • C88.4 Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma]
          • C88.8 Other malignant immunoproliferative diseases
          • C88.9 Malignant immunoproliferative disease, unspecified

Notes

C00-D49

  • Functional activity
  • All neoplasms are classified in this chapter, whether they are functionally active or not. An additional code from Chapter 4 may be used, to identify functional activity associated with any neoplasm.
  • Morphology [Histology]
  • Chapter 2 classifies neoplasms primarily by site (topography), with broad groupings for behavior, malignant, in situ, benign, etc. The Table of Neoplasms should be used to identify the correct topography code. In a few cases, such as for malignant melanoma and certain neuroendocrine tumors, the morphology (histologic type) is included in the category and codes.
  • Primary malignant neoplasms overlapping site boundaries
  • A primary malignant neoplasm that overlaps two or more contiguous (next to each other) sites should be classified to the subcategory/code .8 ('overlapping lesion'), unless the combination is specifically indexed elsewhere. For multiple neoplasms of the same site that are not contiguous, such as tumors in different quadrants of the same breast, codes for each site should be assigned.
  • Malignant neoplasm of ectopic tissue
  • Malignant neoplasms of ectopic tissue are to be coded to the site mentioned, e.g., ectopic pancreatic malignant neoplasms are coded to pancreas, unspecified (C25.9).
    • C25.9 Malignant neoplasm of pancreas, unspecified

Inclusion Terms

C88.3

  • Alpha heavy chain disease
  • Mediterranean lymphoma

Excludes 1

C88

  • B-cell lymphoma, unspecified (C85.1-)
    • C85.1 Unspecified B-cell lymphoma
  • Z85.79 Personal history of other malignant neoplasms of lymphoid, hematopoietic and related tissues

Excludes 2

C81-C96

  • C46.3 Kaposi's sarcoma of lymph nodes
  • secondary and unspecified neoplasm of lymph nodes (C77.-)
    • C77 Secondary and unspecified malignant neoplasm of lymph nodes
  • secondary neoplasm of bone marrow (C79.52)
    • C79.52 Secondary malignant neoplasm of bone marrow
  • secondary neoplasm of spleen (C78.89)
    • C78.89 Secondary malignant neoplasm of other digestive organs