kodex

Kodex

D68.2

Hereditary deficiency of other clotting factors

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Hierarchy

  • D50-D89 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
    • D65-D69 Coagulation defects, purpura and other hemorrhagic conditions (D65-D69)
      • D68 Other coagulation defects
        • D68.0 Von Willebrand disease
        • D68.1 Hereditary factor XI deficiency
        • D68.2 Hereditary deficiency of other clotting factors
        • D68.3 Hemorrhagic disorder due to circulating anticoagulants
        • D68.4 Acquired coagulation factor deficiency
        • D68.5 Primary thrombophilia
        • D68.6 Other thrombophilia
        • D68.8 Other specified coagulation defects
        • D68.9 Coagulation defect, unspecified

Inclusion Terms

D68.2

  • AC globulin deficiency
  • Congenital afibrinogenemia
  • Deficiency of factor I [fibrinogen]
  • Deficiency of factor II [prothrombin]
  • Deficiency of factor V [labile]
  • Deficiency of factor VII [stable]
  • Deficiency of factor X [Stuart-Prower]
  • Deficiency of factor XII [Hageman]
  • Deficiency of factor XIII [fibrin stabilizing]
  • Dysfibrinogenemia (congenital)
  • Hypoproconvertinemia
  • Owren's disease
  • Proaccelerin deficiency

Excludes 1

D68

  • R79.1 Abnormal coagulation profile

Excludes 2

D68

  • coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
    • O08.1 Delayed or excessive hemorrhage following ectopic and molar pregnancy
  • coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
    • O45.0 Premature separation of placenta with coagulation defect
    • O46.0 Antepartum hemorrhage with coagulation defect
    • O67.0 Intrapartum hemorrhage with coagulation defect
    • O72.3 Postpartum coagulation defects

D50-D89

  • autoimmune disease (systemic) NOS (M35.9)
    • M35.9 Systemic involvement of connective tissue, unspecified
  • P00-P96 Certain conditions originating in the perinatal period (P00-P96)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • O00-O9A Pregnancy, childbirth and the puerperium (O00-O9A)
  • Q00-Q99 Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • B20 Human immunodeficiency virus [HIV] disease
  • S00-T88 Injury, poisoning and certain other consequences of external causes (S00-T88)
  • C00-D49 Neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)